Bobble-Head Doll Syndrome in Suprasellar Cysts: Results of Neuroendoscopic Treatment in Four Children


Authors: D. Hořínek 1,4;  J. Schwab 1;  M. Tichý 1;  M. Kynčl 2;  J. Šanda 2;  L. Paulas 3;  M. Vaculík 1;  Z. Novák 5
Authors‘ workplace: Oddělení dětské neurochirurgie FN v Motole, Praha 1;  Klinika zobrazovacích metod 2. LF UK a FN Motol, Praha 2;  Klinika dětské neurologie 2. LF UK a FN Motol, Praha 3;  Ústav patologické fyziologie 2. LF UK, Praha 4;  Neurochirurgická klinika, Fakultní nemocnice u sv. Anny, Brno 5
Published in: Cesk Slov Neurol N 2007; 70/103(1): 88-93
Category: Case Report

Práce byla podpořena granty Ministerstva zdravotnictví ČR IGA ND/7678-3 a IGA NR/7805-2 a VZ 0064203-6308.

Overview

The authors have presented 4 case-reports of children with suprasellar cysts and bobble-head doll syndrome. Obstructive hydrocephalus developed in all the cases given, and severe transient visual disturbance rose in one case. Neuroendoscopic ventriculocystostomy was chosen as a method of therapy in two cases, two other cases underwent neuroendoscopic ventriculocystocisternostomy. A cystoperitoneal shunt was made under neuroendoscopic control in one patient after performing ventriculocystostomy.

The therapy resulted in the cyst decompression in all the patients, clinical symptoms disappeared in 3 cases. Bobble-head doll syndrome is persisting in a boy with a four-year´s delay in diagnosis and therapy.

Bobble-head doll syndrome in suprasellar cysts can be treated successfully using neuroendoscopic ventriculocystostomy or ventriculocystocisternostomy. Bobble-head doll syndrome as a rare syndromological entity has been usually recognized with delay.

Key-words:
bobble-head doll syndrome, suprasellar cysts, neuroendoscopy, diagnostic delay


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Labels
Paediatric neurology Neurosurgery Neurology

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Czech and Slovak Neurology and Neurosurgery

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