Epileptosurgical Solution of Cavernous Hemangioma Associated with Focal Cortical Dysplasia in the Right Temporal Lobe in a Female-Patient with Secondary Epilepsy: a Case Report

Czech version

Authors: H. Ošlejšková ¹; M. Ryzí ¹; M. Brázdil ²; Z. Novák ³; I. Zichová ⁴; J. Skotáková ⁵; V. Mach ⁵
Authors‘ workplace: Klinika dětské neurologie LF MU a FN Brno ¹; I. neurologická klinika LF MU a FN U sv. Anny, Brno ²; Neurochirurgická klinika FN USA a LF MU ³; I. patologicko-anatomický ústav LF MU a FN U sv. Anny, Brno ⁴; Klinika dětské radiologie LF MU a FN Brno ⁵
Published in: Cesk Slov Neurol N 2007; 70/103(3): 316-321
Category: Case Report

Overview

The author has presented a case-report of a 13-year-old girl with cavernous hemangioma situated in the right temporal lobe unusually associated with focal cortical dysplasia and symptomatic epileptic seizures. Having correlated clinical manifestation of the seizures, the brain MRI findings, results of ictal video-EEG and peroperative electrocorticography (ECoG), an epilepsy surgery was carried out –⁠ extended lesionectomy, i.e. removal of a cavernoma, its macroscopically recognizable hemosiderine border and region with epileptic activity in peroperative ECoG that corresponded with the uncus of parahippocampal gyrus and amygdala on the right side. Histological examinations confirmed cavernous hemangioma and focal cortical dysplasia (type IB) in an enlarged resected portion. If compared with other therapeutical solutions, this epileptosurgical approach has improved our patient's chance for long-term post-operative seizure-free life. The girl is now 12 months after the surgery without seizures and without neurological deficit.

Key words:
cavernous hemangioma –⁠ focal cortical dysplasia –⁠ symptomatic epilepsy –⁠ epilepsy of the temporal lobe –⁠ extended lesionectomy –⁠ peroperative corticography

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