Spontaneous intracranial hypotension

Authors: H. Zítek 1;  M. Stratilová 1;  T. Radovnický 1;  A. Sejkorová 1;  L. Hofmann Klzo 2,3;  M. Sameš 1
Authors‘ workplace: Neurochirurgická klinika FZS UJEP, a KZ, a. s. – Masarykovy nemocnice, v Ústí nad Labem, o. z. 1;  Radiologická klinika FN Hradec, Králové 2;  Radiodiagnostické oddělení KZ, a. s. –, Nemocnice Teplice, o. z. 3
Published in: Cesk Slov Neurol N 2022; 85(1): 18-23
Category: Review Article
doi: 10.48095/cccsnn202218


Spontaneous intracranial hypotension (SIH) is a disease in which headache is the main symptom. Recently, it has become an important part of the broad differential diagnosis of causes of headache. Advances in understanding of pathophysiology, indication of proper imaging modalities, and expansion of microsurgical techniques contributed to increased recognition of the disease. Young patients in productive age commonly suffer from SIH, and it might negatively influence both their social and professional life. Therefore, it is of great importance to recognize the symptoms of the disease and treat it properly. The aim of our article is to provide a review of the pathogenesis, current recommendations for the diagnosis and therapy of SIH. A report of a typical case should support our effort.


spontaneous intracranial hypotension – orthostatic headache – cerebrospinal fluid leakage – epidural blood plug


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