Hemangioblastoma of the Cauda Equina – a Case Report


Authors: D. Bludovský 1;  V. Runt 1;  M. Choc 1;  M. Michal 2;  J. Kastner 3
Authors‘ workplace: LF UK a FN Plzeň Neurochirurgické oddělení 1;  LF UK a FN Plzeň Šiklův patologicko-anatomický ústav 2;  LF UK a FN Plzeň Klinika zobrazovacích metod 3
Published in: Cesk Slov Neurol N 2010; 73/106(5): 552-554
Category: Case Report

Overview

Hemangioblastomas are rare lesions, accounting for 1–5% of all spinal cord tumors. ­Seventy-five per cent of them are intramedullary. Lesions of the conus medullaris and the cauda equina are sporadic and typical in von Hippel-Lindau syndrome. We describe the case of a 58-year-old man presenting with radicular pain. Magnetic resonance images revealed a hyperintense tumor of the cauda equina. Surgical intervention consisted of an L2 laminectomy and complete en-bloc resection of a reddish-brown, highly vascular lesion. Histo­pathological study identified it as a hemangioblastoma. Von Hippel-Lindau disease was not proven. The patient is without pain or radicular lesion and without tumor recurrence two years after operation. Although cauda equina hemangioblastoma is a rare cause of lumobischialgia and radiculopathy, we should bear it in mind as a possibility, especially when neurological findings are not typical.

Key words:
hemangioblastoma – cauda equina – von Hippel-Lindau syndrome


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Labels
Paediatric neurology Neurosurgery Neurology

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Czech and Slovak Neurology and Neurosurgery

Issue 5

2010 Issue 5

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