Dysembryoplastic Neuroepithelial Tumor and its Atypical Variant in Children –  Case Reports

Authors: D. Krahulík 1;  M. Vaverka 1;  L. Tučková 2;  M. Köcher 3
Authors‘ workplace: LF UP a FN Olomouc Neurochirurgická klinika 1;  LF UP a FN Olomouc Ústav klinické a molekulární patologie 2;  LF UP a FN Olomouc Radiologická klinika 3
Published in: Cesk Slov Neurol N 2013; 76/109(4): 492-496
Category: Case Report


In this short summary, the authors describe an atypical form of dysembryoplastic neuroepithelial tumor (DNET) in children that has a different clinical, radiological and cytological profile that the typical DNET. Epileptic seizures with good response to radical surgical resection are the main clinical feature of a typical DNET. These tumors are typically in frontal or temporal locations. We describe three patients who underwent surgery during the last eight months, including a girl with an atypical form of DNET presenting with atypical clinical and, mainly, cytogenetic findings.

Key words:
neuroepithelial tumors – atypical forms


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Paediatric neurology Neurosurgery Neurology

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Czech and Slovak Neurology and Neurosurgery

Issue 4

2013 Issue 4

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