Dysembryoplastic Neuroepithelial Tumor and its Atypical Variant in Children – Case Reports

Czech version

Authors: D. Krahulík ¹ ; M. Vaverka ¹; L. Tučková ²; M. Köcher ³
Authors‘ workplace: LF UP a FN Olomouc Neurochirurgická klinika ¹; LF UP a FN Olomouc Ústav klinické a molekulární patologie ²; LF UP a FN Olomouc Radiologická klinika ³
Published in: Cesk Slov Neurol N 2013; 76/109(4): 492-496
Category: Case Report

Overview

In this short summary, the authors describe an atypical form of dysembryoplastic neuroepithelial tumor (DNET) in children that has a different clinical, radiological and cytological profile that the typical DNET. Epileptic seizures with good response to radical surgical resection are the main clinical feature of a typical DNET. These tumors are typically in frontal or temporal locations. We describe three patients who underwent surgery during the last eight months, including a girl with an atypical form of DNET presenting with atypical clinical and, mainly, cytogenetic findings.

Key words:
neuroepithelial tumors – atypical forms

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