Superior semicircular canal dehiscence

Authors: M. Stříteská 1-3;  O. Profant 1,4;  K. Trnková 1;  M. Laboš 5;  J. Weichet 5;  J. Dědková 6;  M. Vališ 7;  V. Chrobok 2;  M. Chovanec 1
Authors‘ workplace: Otorinolaryngologická klinika 3. LF UK a FN Královské Vinohrady, Praha 1;  Klinika otorinolaryngologie a chirurgie hlavy a krku LF UK a FN Hradec Králové 2;  ORL ambulance TINITUS s. r. o., Chrudim 3;  Oddělení neurofyziologie sluchu, Ústav experimentální medicíny, AV ČR, Praha 4;  Radiodiagnostická klinika 3. LF UK a FN Královské Vinohrady, Praha 5;  Radiologická klinika LF UK a FN Hradec Králové 6;  Neurologická klinika LF UK a FN Hradec Králové 7
Published in: Cesk Slov Neurol N 2019; 82(4): 461-463
Category: Letter to editor
doi: 10.14735/amcsnn2019461


Syndrome of superior semicircular canal dehiscence represents relatively rare disease of the inner ear. It presents with various combinations of often bizarre vestibular and hearing symptoms. The pathological and pathophysiological basis of this clinical syndrome is defect of otic capsule in the middle fossa. Dehiscence represents the third mobile window of the otic capsule. The purpose of the case report is to present characteristic neurootologic and audiologic symptomatology of the syndrome, key steps in its diagnosis and its surgical management.

The authors declare they have no potential conflicts of interest concerning drugs, products, or services used in the study.

The Editorial Board declares that the manu script met the ICMJE “uniform requirements” for biomedical papers.


superior semicircular canal dehiscence – Tullio phenomenon – vestibular evoked myogenic potentials – third window


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Paediatric neurology Neurosurgery Neurology

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